The total choledochal cyst excision, with Roux-en-Y hepaticojejunostomy is effective in the treatment of congenital choledochal cyst.

囊肿全切除、肝管空肠鲁氏Y形吻合应作为胆总管囊种的首选术式。

Conclusions： The abnormal distribution of NGFR in the aganglionic choledochal suggests involvement of NGFR in the CCC.

NGFR在先天性胆总管囊肿的异常分布可能与CCC的发病机理有关。